Pancreatoblastoma
Pancreatoblastoma
Definition
Pancreatoblastoma is a rare malignant epithelial pancreatic neoplasm, most often found in children, which usually presents with the non-specific symptoms of a palpable mass, vomiting abdominal pain, jaundice, and weight loss/failure to thrive, and is characterized histologically by multiple lines of differentiation (acinar, ductal, mesenchymal, neuroendocrine) and the presence of squamoid nests.
Also known as pancreatoblastoma (morphologic abnormality) — per MONDO
Also identified as
- DOID 6823 per MONDO
- MESH C537162 per MONDO
- NCIT C4265 per MONDO
- Orphanet 677 per MONDO
- UMLS C0334489 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Alimentary part of gastrointestinal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Exocrine pancreas | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Pancreas | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |