Hereditary spastic paraplegia
ICD-10 Code
G11.4
Hereditary spastic paraplegia
Definition
Hereditary spastic paraplegias (HSP) comprise a genetically and clinically heterogeneous group of neurodegenerative disorders characterized by progressive spasticity and hyperreflexia of the lower limbs.
Also known as familial spastic paraplegia, hereditary spastic paraparesis, HSP, SPG, Strümpell-Lorrain disease — per MONDO
Also identified as
- DOID 2476 per MONDO
- ICD10CM G11.4 per MONDO
- ICD9 334.1 per MONDO
- MESH D015419 per MONDO
- NCIT C140267 per MONDO
- Orphanet 685 per MONDO
- SCTID 39912006 per MONDO
- UMLS C0037773 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Central nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |