Post-transplant lymphoproliferative disease
ICD-10 Code
D47.Z1
Post-transplant lymphoproliferative disease
Definition
Post-transplant lymphoproliferative disorder (PTLD) is a polyclonal (benign) or clonal (malignant) proliferation of lymphoid cells that develops as a consequence of immunosuppression in a recipient of a solid organ or bone marrow allograft. PTLDs comprise a spectrum ranging from early, Epstein-Barr virus (EBV)-driven polyclonal lymphoid proliferations to EBV-positive or EBV- negative lymphomas of predominantly B-cell or less often T-cell type. (WHO, 2001)
Also known as post-transplant lymphoproliferative disorder, PTLD — per MONDO
Also identified as
- ICD10CM D47.Z1 per MONDO
- NCIT C4727 per MONDO
- Orphanet 70568 per MONDO
- SCTID 254290004 per MONDO
- UMLS C0432487 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Lymphoid system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |