Polyarteritis nodosa
ICD-10 Code
M30.0
Polyarteritis nodosa
Definition
Polyarteritis nodosa (PAN) is a rare, clinically heterogeneous, rheumatologic disease characterized by necrotizing inflammatory lesions affecting small- and medium-sized blood vessels. PAN most commonly affects skin, joints, peripheral nerves, the gut, and the kidney.
Also known as classic polyarteritis nodosa, classical polyarteritis nodosa, Küssmaul-Maier disease, PAN, panarteritis nodosa, periarteritis nodosa, polyarteritis nodosa — per MONDO
Also identified as
- DOID 9810 per MONDO
- ICD10CM M30.0 per MONDO
- ICD9 446.0 per MONDO
- MESH D010488 per MONDO
- NCIT C26847 per MONDO
- Orphanet 767 per MONDO
- SCTID 155441006 per MONDO
- UMLS C0031036 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Artery | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |