Familial long QT syndrome
Familial long QT syndrome
Definition
A hereditary cardiac disease characterized by a prolongation of the QT interval at basal ECG and by a high risk of life-threatening arrhythmias.
Also known as congenital long QT syndrome, familial long QT syndrome, hereditary long QT syndrome, LQTS, Romano-Ward long QT syndrome, Romano-Ward syndrome, Ward-Romano syndrome — per MONDO