Hereditary hemorrhagic telangiectasia
ICD-10 Code
I78.0
Hereditary hemorrhagic telangiectasia
Definition
A disorder of angiogenesis leading to arteriovenous dilatations: cutaneo-mucosal hemorrhagic telangiectasias and visceral shunting.
Also known as hereditary hemorrhagic telangiectasia, HHT, Osler-Weber-Rendu disease, Rendu-Osler disease, Rendu-Osler-Weber disease, telangiectasia, hereditary Hemorrahagic, of Rendu, Osler, telangiectasia, hereditary hemorrhagic — per MONDO
Also identified as
- DOID 1270 per MONDO
- ICD10CM I78.0 per MONDO
- ICD9 448.0 per MONDO
- MESH D013683 per MONDO
- NCIT C35064 per MONDO
- Orphanet 774 per MONDO
- SCTID 21877004 per MONDO
- UMLS C0039445 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Cardiovascular system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |