Cutaneous neuroendocrine carcinoma

ICD-10 Code C4A

Cutaneous neuroendocrine carcinoma

Definition

Cutaneous neuroendocrine carcinoma is a primary cutaneous cancer arising from a subset of skin neuroendocrine cells (Merkel cells, giving the name Merkel cell carcinoma (MCC)).

Also known as carcinoma of Merkel cell, cutaneous APUDoma, cutaneous neuroendocrine carcinoma, MCC, Merkel cell cancer, Merkel Cell Carcinoma, Merkel cell tumor, Merkel cell tumour, neuroendocrine carcinoma of skin, neuroendocrine carcinoma of the skin, neuroendocrine skin carcinoma, trabecular cancer, trabecular skin carcinoma — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Endocrine gland Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Endocrine gland Disease Has Primary Anatomic Site NCIT · CC BY 4.0

Drugs indicated

Drug Relation Source
Avelumab may treat MEDRT · Public domain (U.S. Government work)
Pembrolizumab may treat MEDRT · Public domain (U.S. Government work)
Retifanlimab may treat MEDRT · Public domain (U.S. Government work)