SAPHO syndrome

SAPHO syndrome

Definition

SAPHO syndrome (acronym for Synovitis, Acne, Pustulosis, Hyperostosis and Osteitis) is an auto-inflammatory disease, mainly characterized by the association of neutrophilic cutaneous involvement and chronic osteomyelitis.

Also known as PPHS, Pustulo-psoriatic hyperostotic Spondyloarthritis, synovitis-acne-pustulosis-hyperostosis-osteitis syndrome, synovitis, acne, pustulosis, hyperostosis, and osteitis syndrome — per MONDO

Also identified as