Congenital non-bullous ichthyosiform erythroderma
Congenital non-bullous ichthyosiform erythroderma
Definition
A variant of autosomal recessive congenital ichthyosis (ARCI), a rare epidermal disease, characterized by fine, whitish scales on a background of erythematous skin over the whole body.
Also known as alligator skin, CIE, congenital ichthyosiform erythroderma, congenital ichthyosiform erythroderma (disease), congenital non bullous ichthyosiform erythroderma, erythrodermic ichthyosis, ichthyosiform erythroderma, non-bullous congenital ichthyosiform erythroderma, nonbullous congenital ichthyosiform erythroderma — per MONDO