Junctional epidermolysis bullosa inversa
Junctional epidermolysis bullosa inversa
Definition
Junctional epidermolysis bullosa inversa is a rare severe subtype of junctional epidermolysis bullosa (JEB) characterized by blistering and erosions confined to intertriginous skin sites, the esophagus, and vagina.
Also known as EBJ-I, inverse JEB, JEB-I — per MONDO