Pemphigus erythematosus
ICD-10 Code
L10.4
Pemphigus erythematosus
Definition
Pemphigus erythematosus is a rare superficial pemphigus disease characterized clinically by well-demarcated, localized, erythematous, scaly, hyperkeratotic, crusted plaques, with frequent butterfly distribution over the malar area of the face (but also commonly involving trunk and scalp, and less frequently the extremities, with a photoexposed distribution). Histologically, granular deposits along the dermal-epidermal junction, in addition to intercellular deposition in the upper epidermis, are observed.
Also known as seborrheic pemphigus, Senear-Usher syndrome — per MONDO