Desmoplastic small round cell tumor
Desmoplastic small round cell tumor
Definition
Desmoplastic small round cell tumor (DSRCT) is an aggressive soft tissue cancer that typically arises in serous lined surfaces of the abdominal or pelvic peritoneum, and spreads to the omentum, lymph nodes and hematogenously disseminates especially to the liver. Extraserous primary location has been reported in exceptional cases.
Also known as Desmoplas. small round cell tumor, Desmoplas. small round cell tumour, Desmoplastic small round cell tumor, Desmoplastic small round cell tumour, Desmoplastic small round-cell neoplasm, Desmoplastic small round-cell tumor, Desmoplastic small round-cell tumour, DSRCT, Polyphenotypic small round cell tumor, Polyphenotypic small round cell tumour — per MONDO