Susac syndrome
Susac syndrome
Definition
Susac syndrome (SS) is a rare disorder characterized by the triad of central nervous system (CNS) dysfunction, branch retinal artery occlusions (BRAOs) and sensorineural hearing loss (SNHL). It is presumably due to autoimmune-mediated occlusions of microvessels in the CNS, the retina, and the inner ear.
Also known as RED-M, Retinocochleocerebral vasculopathy, retinopathy-encephalopathy-deafness associated with microangiopathy, SICRET syndrome, small infarctions of cochlear, retinal and encephalic tissue — per MONDO