B-cell prolymphocytic leukemia
B-cell prolymphocytic leukemia
Definition
A neoplasm of prolymphocytes affecting the blood, bone marrow, and spleen. It is characterized by prolymphocytes exceeding 55% of the lymphoid cells in the blood and profound splenomegaly.
Also known as B prolymphocytic leukaemia, B prolymphocytic leukemia, B-cell prolymphocytic leukemia, B-PLL — per MONDO
Also identified as
- DOID 0081041 per MONDO
- MESH D054403 per MONDO
- NCIT C4753 per MONDO
- Orphanet 86852 per MONDO
- SCTID 277619001 per MONDO
- UMLS C0475801 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Bone marrow | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Lymphoid system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |