Splenic marginal zone lymphoma
Splenic marginal zone lymphoma
Definition
Splenic marginal zone lymphoma is a rare, indolent B-cell non-Hodgkin lymphoma characterized by abnormal clonal proliferation of mature B-lymphocytes with involvement in the spleen, bone marrow and, frequently, the blood. It usually presents with splenomegaly, lymphocytosis, anemia and/or thrombocytopenia. Hepatitis C virus and autoimmune manifestations, such as autoimmune hemolytic anemia and autoimmune thrombocytopenia, could be associated.
Also known as marginal zone lymphoma of spleen, marginal zone lymphoma of the spleen, SLVL, SMZL, splenic lymphoma with circulating villous lymphocytes, splenic marginal zone B-cell lymphoma, splenic marginal zone B-cell lymphoma with villous lymphocytes, splenic marginal zone lymphoma, splenic marginal zone lymphoma with villous lymphocytes — per MONDO
Also identified as
- DOID 0050750 per MONDO
- NCIT C4663 per MONDO
- Orphanet 86854 per MONDO
- SCTID 763666008 per MONDO
- UMLS C0349632 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Lymphoid system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Spleen | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Spleen | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |