Heavy chain disease
ICD-10 Code
C88.2
Heavy chain disease
Definition
Heavy-chain diseases (HCDs) are rare monoclonal lymphoplasma-cell proliferative disorders involving B cells and are characterized by the synthesis of truncated heavy chains without associated light chains.
Also known as HCD, heavy chain disease — per MONDO
Also identified as
- DOID 0060125 per MONDO
- ICD10CM C88.2 per MONDO
- ICD10CM C88.3 per MONDO
- ICD9 273.2 per MONDO
- MESH D006362 per MONDO
- NCIT C3082 per MONDO
- Orphanet 86864 per MONDO
- SCTID 68979007 per MONDO
- UMLS C0018852 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Lymphoid system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |