Hepatosplenic T-cell lymphoma

ICD-10 Code C86.1

Hepatosplenic T-cell lymphoma

Definition

An extranodal, mature T-cell non-Hodgkin lymphoma that originates from cytotoxic T-cells, usually of gamma/delta T-cell type. It is characterized by the presence of medium-size neoplastic lymphocytes infiltrating the hepatic sinusoids. A similar infiltrating pattern is also present in the spleen and bone marrow that are usually involved at the time of the diagnosis.

Also known as Hepatosplenic gamma/Delta T-cell lymphoma — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Alimentary part of gastrointestinal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Alimentary part of gastrointestinal system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Bone marrow Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Liver Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Liver Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Lymphoid system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Spleen Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Spleen Disease Has Primary Anatomic Site NCIT · CC BY 4.0