Subcutaneous panniculitis-like T-cell lymphoma
ICD-10 Code
C86.3
Subcutaneous panniculitis-like T-cell lymphoma
Definition
Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is a rare cytotoxic cutaneous lymphoma that has been recognized as a distinct subset of peripheral T-cell lymphomas originating and presenting primarily in the subcutaneous fat tissue.
Also known as SPTCL, subcutaneous panniculitic T-cell lymphoma, subcutaneous panniculitis-like T-cell lymphoma, subcutaneous panniculitis-like T-cell lymphoma (Alpha/Beta type), subcutaneous panniculitis-like T-cell lymphoma, Alpha/Beta type — per MONDO
Also identified as
- DOID 0070662 per MONDO
- ICD10CM C86.3 per MONDO
- ICD9 202.70 per MONDO
- MESH C537503 per MONDO
- NCIT C6918 per MONDO
- OMIM 618398 per MONDO
- Orphanet 86884 per MONDO
- SCTID 404133000 per MONDO
- UMLS C0522624 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Hypodermis | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Integumental system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Lymphoid system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Skin of body | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Skin of body | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |