Langerhans cell sarcoma

Definition

A neoplastic proliferation of Langerhans cells with overtly malignant cytologic features. It can be considered a higher grade variant of Langerhans cell histiocytosis (LCH) and it can present de novo or progress from antecedent LCH. (WHO, 2001)

Also known as Langerhans cell sarcoma, sarcoma of Langerhans cell — per MONDO

Also identified as

• DOID 7146 per MONDO
• MESH D054752 per MONDO
• NCIT C6921 per MONDO
• Orphanet 86897 per MONDO
• SCTID 724649000 per MONDO
• UMLS C1260327 per MONDO