Hepatic veno-occlusive disease
ICD-10 Code
K76.5
Hepatic veno-occlusive disease
Definition
Hepatic veno-occlusive disease (hepatic VOD) is a condition resulting from toxic injury to the hepatic sinusoidal capillaries that leads to obstruction of the small hepatic veins.
Also known as Budd Chiari Syndrome, hepatic Vod, liver veno-occlusive disease, sinusoidal obstruction syndrome — per MONDO
Also identified as
- DOID 0080177 per MONDO
- ICD10CM K76.5 per MONDO
- ICD9 453.89 per MONDO
- MESH D006504 per MONDO
- NCIT C26793 per MONDO
- Orphanet 890 per MONDO
- SCTID 65617004 per MONDO
- UMLS C0019156 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Alimentary part of gastrointestinal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Blood vessel | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Liver | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Liver | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
Drugs indicated
| Drug | Relation | Source |
|---|---|---|
| Defibrotide | may treat | MEDRT · Public domain (U.S. Government work) |