Capillary leak syndrome
Capillary leak syndrome
Definition
A syndrome characterized by leakage of intravascular fluids into the extravascular space. This syndrome is observed in patients who demonstrate a state of generalized leaky capillaries following shock syndromes, low-flow states, ischemia-reperfusion injuries, toxemias, medications, or poisoning. It can lead to generalized edema and multiple organ failure.
Also known as acute vascular leak syndrome, AVLS, capillary hyperpermeability syndrome, capillary leak syndrome, Clarkson disease, CLS, idiopathic capillary leak syndrome, SCLS, Systemic Capillary Leak Syndrome — per MONDO
Also identified as
- DOID 14400 per MONDO
- ICD9 448.9 per MONDO
- MESH D019559 per MONDO
- NCIT C62578 per MONDO
- Orphanet 188 per MONDO
- SCTID 87730004 per MONDO
- UMLS C0343084 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Capillaries | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |