Hereditary angioedema
Hereditary angioedema
Definition
Hereditary angioedema (HAE) is a genetic disease characterized by the occurrence of transitory and recurrent subcutaneous and/or submucosal edemas resulting in swelling and/or abdominal pain.
Also known as familial angioneurotic edema, familial angioneurotic oedema, HAE, hereditary angioedema, hereditary angioneurotic edema, hereditary angioneurotic oedema, hereditary bradykinine-induced angioedema, hereditary non histamine-induced angioedema — per MONDO
Also identified as
- DOID 14735 per MONDO
- MESH D054179 per MONDO
- NCIT C84758 per MONDO
- Orphanet 91378 per MONDO
- SCTID 82966003 per MONDO
- UMLS C0019243 per MONDO
Drugs indicated
| Drug | Relation | Source |
|---|---|---|
| Garadacimab | may prevent | MEDRT · Public domain (U.S. Government work) |
| Lanadelumab | may prevent | MEDRT · Public domain (U.S. Government work) |
| Icatibant | may treat | MEDRT · Public domain (U.S. Government work) |