Acquired thrombotic thrombocytopenic purpura

Definition

Acquired thrombotic thrombocytopenic purpura is the non-hereditary form of thrombotic thrombocytopenic purpura (TTP), characterized by profound peripheral thrombocytopenia, microangiopathic hemolytic anemia (MAHA) and single or multiple organ failure of variable severity.

Also known as acquired ADAMTS13 deficiency, acquired thrombotic thrombocytopenic purpura, acquired TTP, autoimmune thrombotic thrombocytopenic purpura — per MONDO

Also identified as

• MESH C536901 per MONDO
• NCIT C131653 per MONDO
• Orphanet 93585 per MONDO
• SCTID 438476003 per MONDO
• UMLS C2584778 per MONDO

Affected Organs