Autoimmune enteropathy

Autoimmune enteropathy

Definition

Severe-immune mediated enteropathy describes a variety of intestinal disorders that can range from a serious, early-onset systemic disease (IPEX) to a mild isolated gastrointestinal disease. In children it manifests with severe diarrhea and dehydration in the presence of characteristic antibodies (anti-enterocyte and anti-goblet cell) and in adults with chronic diarrhea, malabsorption and weight loss.

Also known as immune-mediated protracted diarrhea of infancy, immune-mediated protracted diarrhoea of infancy, severe immune-mediated enteropathy — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Alimentary part of gastrointestinal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Alimentary part of gastrointestinal system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Intestine Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Intestine Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Small intestine Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Small intestine Disease Has Primary Anatomic Site NCIT · CC BY 4.0