Eisenmenger syndrome
ICD-10 Code
I27.83
Eisenmenger syndrome
Definition
Eisenmenger syndrome (ES) is an form of pulmonary arterial hypertension (PAH) associated with unoperated congenital heart disease and is characterized by congenital heart malformations with reversed or bi-directional shunting through an intra-cardiac or intervascular (usually aorto-pulmonary) communication with the development of PAH.
Also known as Eisenmenger's syndrome — per MONDO