Pancreatic neuroendocrine tumor

Definition

Pancreatic endocrine tumor, also known as pancreatic neuroendocrine tumor (PNET), describes a group of endocrine tumors originating in the pancreas that are usually indolent and benign, but may have the potential to be malignant. They can be functional, exhibiting a hormonal hypersecretion syndrome, but can be non-functional presenting with non-specific symptoms and include insulinoma, glucagonoma, VIPoma, somatostatinoma (SSoma), PPoma and Zollinger-Ellison syndrome (ZES, or gastrinoma) and other ectopic hormone producing tumors (such as GRFoma).

Also known as islet cell tumor, islet cell tumors - pancreas, islet cell tumors of the pancreas, islet cell tumour, islet cell tumours - pancreas, islet cell tumours of the pancreas, pancreatic NET, pancreatic neuroendocrine tumor, well differentiated pancreatic endocrine neoplasm, well differentiated pancreatic endocrine tumor, well differentiated pancreatic endocrine tumour, well-differentiated NEN of pancreas, well-differentiated neuroendocrine neoplasm of pancreas, well-differentiated pancreatic NEN, well-differentiated pancreatic neuroendocrine neoplasm — per MONDO

Also identified as

• NCIT C27720 per MONDO
• Orphanet 97253 per MONDO
• UMLS C1337011 per MONDO

Affected Organs