VIPoma

Definition

VIPoma is an extremely rare type of pancreatic neuroendocrine tumor that secretes vasoactive intestinal polypeptide (VIP) leading to the manifestations of watery diarrhea, hypokalemia and achlorhydia or hypochhlorhydia (known as WDHA syndrome).

Also known as Diarrheogenic islet cell tumor, Diarrheogenic islet cell tumour, malignant vasoactive intestinal peptide-secreting tumour, vasoactive intestinal peptide producing neoplasm, vasoactive intestinal peptide producing tumor, vasoactive intestinal peptide producing tumour, vasoactive intestinal peptide secreting neoplasm, vasoactive intestinal peptide-secreting tumour, Verner-Morrison syndrome, VIP producing neoplasm, VIP- secreting neoplasm, VIP- secreting tumor, VIP- secreting tumour, VIP-producing NET, VIP-producing neuroendocrine tumor, VIP-producing neuroendocrine tumour, VIP-secreting tumor, VIP-secreting tumour, VIPoma — per MONDO

Also identified as

• DOID 5574 per MONDO
• ICD9 239.7 per MONDO
• MESH D003969 per MONDO
• NCIT C26749 per MONDO
• Orphanet 97282 per MONDO
• SCTID 253005002 per MONDO
• UMLS C0011993 per MONDO

Affected Organs