Non-amyloid fibrillary glomerulopathy
Non-amyloid fibrillary glomerulopathy
Definition
Non-amyloid fibrillary glomerulopathy (non-amyloid FGP) is a rare cause of glomerulonephritis (GN) characterized by glomerular accumulation of non-amyloid fibrils in the mesangium and the glomerular (and rarely tubular) basement membrane, that mainly presents with renal insufficiency, micro-hematuria and nephrotic range proteinuria. Non-amyloid FGP and immunotactoid glomerulopathy (ITG) are often grouped together as pathogenetically related diseases.
Also known as Congo red-negative amyloidosis-like glomerulopathy, Fibrillary Glomerulonephritis, non-amyloid fibrillary glomerulonephritis — per MONDO