Ehlers-Danlos syndrome

ICD-10 Code Q79.6

Ehlers-Danlos syndrome

Definition

The Ehlers–Danlos syndromes (EDS) are a clinically and genetically heterogeneous group of heritable connective tissue disorders (HCTDs) characterized by joint hypermobility, skin hyperextensibility, and tissue fragility.

Also known as Danlos disease, Danlos Disease, Ehlers, danlos ehlers syndrome, Disease, Ehlers Danlos, Disease, Ehlers-Danlos, Dystrophia mesodermalis congenita, EDS, Ehler Danlos Syndrome, Ehlers Danlos Disease, Ehlers Danlos Syndrome, Ehlers-Danlos Disease, Ehlers-Danlos syndromes, elastic skin, Fibrodysplasia elastica generalisata, Hereditary collagen dysplasia, Meekeren-Ehlers-Danlos syndrome, skin elastic, Syndrome, Ehlers-Danlos — per MONDO

Also identified as