Shone complex
Shone complex
Definition
A congenital cardiovascular abnormality characterized by the presence of subvalvar left ventricular outflow tract obstruction, coarctation of the aorta, and mitral stenosis.
Also known as shone syndrome, shone's syndrome (greater than 3 sites) — per MONDO
Also identified as
- ICD9 746.84 per MONDO
- NCIT C99058 per MONDO
- Orphanet 99063 per MONDO
- SCTID 41371000119100 per MONDO
- UMLS C1868705 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Cardiovascular system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |