Persistent left superior vena cava connecting to the left-sided atrium
Persistent left superior vena cava connecting to the left-sided atrium
Definition
Persistent left superior vena cava connecting to the left-sided atrium is a rare, congenital vascular malformation of the major vessels characterized by a persistent left superior vena cava which drains directly to the left atrium, without passing through the coronary sinus (that may be absent in some cases). Patients are usually asymptomatic and discovered incidentally, however hypoxia, cyanosis, murmurs, palpitations, cardiac structural anomalies (e.g. atrial septal defect, bicuspid aortic valve, cor triatrium) and risk of paradoxical embolization may be associated.
Also known as left superior caval vein persisting to the left-sided atrium, persistent left superior caval vein connecting to the left-sided atrium, persistent left SVC connecting to the left-sided atrium — per MONDO