Right superior vena cava connecting to left-sided atrium
Right superior vena cava connecting to left-sided atrium
Definition
Right superior vena cava connecting to the left-sided atrium is a rare, congenital vascular malformation of the major vessels characterized by the right SVC passing medially and dorsally to the aortic root and draining into the left atrium. Patients usually present a right-to-left systemic venous blood shunt which may manifest with arterial hypoxemia, cyanosis, exercise dyspnea, clubbing of the fingers, palpitations, murmurs and/or potentially fatal brain abscess. Association with other cardiac anomalies has been reported.
Also known as right superior caval vein connecting to left-sided atrium, right SVC connecting to left-sided atrium — per MONDO