Pigmented dermatofibrosarcoma protuberans
Pigmented dermatofibrosarcoma protuberans
Definition
A morphologic variant of dermatofibrosarcoma protuberans characterized by the presence of melanin-pigmented dendritic cells.
Also known as bednar tumor, bednar tumour, pigmented dermatofibrosarcoma protuberans, pigmented dermatofibrosarcoma protuberans (bednar tumor) — per MONDO
Also identified as
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Dermis | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Integumental system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Skin of body | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Skin of body | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |