Cutaneous undifferentiated pleomorphic sarcoma
Cutaneous undifferentiated pleomorphic sarcoma
Definition
An undifferentiated pleomorphic sarcoma arising from the skin. It is characterized by the presence of spindle cells in a storiform pattern and histiocytes with abundant cytoplasm.
Also known as cutaneous malignant fibrous histiocytoma, cutaneous unclassified pleomorphic sarcoma, cutaneous unclassified pleomorphic sarcoma (formerly cutaneous "malignant fibrous histiocytoma"), cutaneous unclassified pleomorphic sarcoma (formerly cutaneous "MFH"), cutaneous unclassified pleomorphic sarcoma (formerly cutaneous), cutaneous undifferentiated pleomorphic sarcoma, malignant cutaneous fibrous histiocytoma, malignant fibrous histiocytoma of skin, malignant fibrous histiocytoma of the skin, malignant skin fibrous histiocytoma, undifferentiated pleomorphic sarcoma of zone of skin, zone of skin undifferentiated pleomorphic sarcoma — per MONDO
Also identified as
- DOID 1906 per MONDO
- ICD9 171.9 per MONDO
- NCIT C5576 per MONDO
- SCTID 404014008 per MONDO
- UMLS C1275254 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Dermis | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Integumental system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Skin of body | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Skin of body | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |