Creutzfeldt-Jakob disease
ICD-10 Code
A81.0
Category
Neurological
Creutzfeldt-Jakob disease
Definition
A rare transmittable degenerative disorder of the brain caused by prions. Morphologically it is characterized by spongiform degeneration of the cerebral and cerebellar cortex. Signs and symptoms include sleep disturbances, personality changes, aphasia, ataxia, muscle atrophy and weakness, visual loss, and myoclonus. It usually leads to death within a year from the onset of the disease.
Also known as CJD, CJD (Creutzfeldt Jakob disease), classic Creutzfeldt-Jakob disease, Creutzfeldt Jakob Disease, Creutzfeldt-Jacob disease, Jakob-Creutzfeldt disease — per MONDO
Also identified as
- DOID 11949 per MONDO
- ICD9 046.1 per MONDO
- ICD9 046.19 per MONDO
- MESH D007562 per MONDO
- NCIT C26802 per MONDO
- SCTID 792004 per MONDO
- UMLS C0022336 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Brain | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Brain | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |