Solid pseudopapillary neoplasm of the pancreas
Solid pseudopapillary neoplasm of the pancreas
Definition
A low-grade malignant neoplasm that arises from the exocrine pancreas. It is characterized by the presence of uniform cells that form solid and pseudopapillary patterns, cystic changes, and hemorrhage. Perineural invasion, vascular invasion, and invasion into surrounding tissues may be present. It usually presents as an encapsulated, solitary, and lobulated pancreatic mass. It is usually found incidentally during physical examination or it may present with abdominal discomfort and pain. It occurs predominantly in young women. Complete removal of the tumor is curative in the majority of cases.
Also known as Frantz tumor, Frantz tumour, solid pseudopapillary neoplasm of the pancreas, solid pseudopapillary tumor of the pancreas, solid pseudopapillary tumour of the pancreas — per MONDO
Also identified as
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Alimentary part of gastrointestinal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Exocrine pancreas | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Pancreas | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |