Major salivary gland adenoid cystic carcinoma

Major salivary gland adenoid cystic carcinoma

Definition

An aggressive carcinoma that arises from the major salivary glands. It is characterized by the presence of malignant epithelial and myoepithelial cells forming cribriform, tubular, and solid patterns. It usually presents as a slow growing mass. Patients develop pain because of the tendency of these carcinomas to invade perineural tissues.

Also known as adenoid cystic carcinoma of major salivary gland, adenoid cystic carcinoma of the major salivary gland, major salivary gland adenoid cystic cancer, major salivary gland adenoid cystic carcinoma — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Craniocervical region Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Craniocervical region Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Major salivary gland Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Major salivary gland Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Saliva-secreting gland Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Saliva-secreting gland Disease Has Primary Anatomic Site NCIT · CC BY 4.0