Permanent neonatal diabetes mellitus

Permanent neonatal diabetes mellitus

Definition

Permanent neonatal diabetes mellitus (PNDM) is a monogenic form of neonatal diabetes (NDM) characterized by persistent hyperglycemia within the first 12 months of life in general, requiring continuous insulin treatment.

Also known as monogenic diabetes of infancy, PNDM — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Alimentary part of gastrointestinal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Alimentary part of gastrointestinal system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Endocrine gland Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Pancreas Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Pancreas Disease Has Primary Anatomic Site NCIT · CC BY 4.0