Paroxysmal familial ventricular fibrillation
Paroxysmal familial ventricular fibrillation
Definition
A rare, genetic, cardiac rhythm disease characterized by ventricular fibrillation in the absence of any structural or functional heart disease, or known repolarization abnormalities. The presence of J waves is associated with a higher risk of nocturnal ventricular fibrillation events and a higher risk of recurrence.
Also known as idiopathic ventricular fibrillation, idiopathic ventricular fibrillation, non Brugada type, IVF, paroxysmal familial ventricular fibrillation, paroxysmal familial ventricular fibrillation (disorder), paroxysmal ventricular fibrillation, ventricular fibrillation, paroxysmal familial — per MONDO