Paroxysmal nocturnal hemoglobinuria
ICD-10 Code
D59.5
Paroxysmal nocturnal hemoglobinuria
Definition
Paroxysmal nocturnal hemoglobinuria (PNH) is an acquired clonal hematopoietic stem cell disorder characterized by corpuscular hemolytic anemia, bone marrow failure and frequent thrombotic events.
Also known as acquired paroxysmal nocturnal hemoglobinuria, hereditary paroxysmal nocturnal hemoglobinuria, inherited paroxysmal nocturnal hemoglobinuria, Marchiafava-Micheli disease, paroxysmal hemoglobinuria, PNH — per MONDO