Butterfly-shaped pigment dystrophy
Butterfly-shaped pigment dystrophy
Definition
A patterned dystrophy of the retinal pigment epithelium characterized by abnormal accumulation of lipofuscin in a butterfly-shaped distribution at the retinal pigment epithelium level. Patients manifest with a slowly progressive loss of vision that often only becomes apparent in old age.
Also known as butterfly-shaped pattern dystrophy, butterfly-shaped pigment dystrophy, butterfly-shaped pigmentary macular dystrophy — per MONDO