Vanishing lung syndrome

Vanishing lung syndrome

Definition

A rare form of irreversible damage to the pulmonary parenchyma often due to chronic obstructive pulmonary disease (COPD). It is associated with a spectrum of clinical manifestations, including worsening dyspnea, cough, declining pulmonary function, and occasionally spontaneous pneumothorax due to ruptured bullae.

Also known as idiopathic giant bullous emphysema, VLS — per MONDO