Developmental and/or epileptic encephalopathy with spike-wave activation in sleep
Developmental and/or epileptic encephalopathy with spike-wave activation in sleep
Definition
A rare epileptic encephalopathy of childhood characterized by seizures, an electroencephalographic (EEG) pattern of electrical status epilepticus in sleep (ESES) and neurocognitive regression in at least 2 domains of development. This syndrome encompasses the previous syndromes epileptic encephalopathy with continuous spike-wave in sleep and atypical childhood epilepsy with centrotemporal spikes (also previously known as pseudo-Lennox syndrome and atypical benign partial epilepsy).
Also known as continuous slow spike and wave of sleep, continuous spike-wave during slow sleep syndrome, continuous spike-wave in sleep, continuous spikes and waves during sleep, continuous spikes and waves during slow-wave sleep, CSWS, CSWSS syndrome, DEE-SWAS, developmental and epileptic encephalopathy with spike-wave activation in sleep, EE-SWAS, EESWAS, electrical status epilepticus of sleep, electrographic status epilepticus in sleep, electrographic status epilepticus of sleep, epileptic aphasia, epileptic encephalopathy with continuous spike-and-wave during slow sleep, epileptic encephalopathy with spike and wave activation in sleep, epileptic encephalopathy with spike-and-wave activation in sleep, eses index, ESES with language regression, LK syndrome, LKS — per MONDO