Cardiac conduction disease with or without cardiomyoopathy

Cardiac conduction disease with or without cardiomyoopathy

Definition

A rare genetic cardiac disease characterized by variably expressed atrial tachyarrhythmia (such as atrial flutter, paroxysmal or chronic atrial fibrillation, ectopic atrial tachycardia, or multifocal atrial tachycardia), infra-Hisian conduction system disease, and vulnerability to dilated cardiomyopathy. Age of onset ranges between childhood and adulthood.

Also known as hereditary atrial tachyarrhythmia-infra-Hisian cardiac conduction disease — per MONDO

Also identified as