Hemihydranencephaly

Hemihydranencephaly

Definition

A rare congenital brain disorder characterized by complete or almost near-complete unilateral absence of the cortical cortex, which is filled by a sac of cerebrospinal fluid. The presumed cause is a prenatal vascular disruption with occlusion of the carotid artery territories ipsilateral to the damaged brain.

Also known as hemi-hydranencephaly — per MONDO

Also identified as