Long QT syndrome

ICD-10 Code I45.81

Long QT syndrome

Definition

A condition that is characterized by episodes of fainting (syncope) and varying degree of ventricular arrhythmia as indicated by the prolonged QT interval. The inherited forms are caused by mutation of genes encoding cardiac ion channel proteins. The two major forms are Romano-Ward syndrome (also known as long QT syndrome 1) and Jervell-Lange Nielsen syndrome.

Also known as long QT syndrome, ventricular arrhythmia associated with long QT syndrome — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Cardiovascular system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Cardiovascular system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Heart Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Heart Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Respiratory system Disease Has Associated Anatomic Site NCIT · CC BY 4.0