Botryoid rhabdomyosarcoma
Botryoid rhabdomyosarcoma
Definition
A morphologic variant of embryonal rhabdomyosarcoma arising from organs with a mucosal epithelial surface. It is characterized by the formation of a cambium layer in the affected tissue and polypoid nodules within an abundant myxoid stroma.
Also known as botryoid sarcoma, botryoid sarcoma (morphologic abnormality), botryoid-type embryonal rhabdomyosarcoma, sarcoma botryoides — per MONDO
Also identified as
- DOID 3255 per MONDO
- ICD9 171.9 per MONDO
- NCIT C9150 per MONDO
- SCTID 404052009 per MONDO
- UMLS C1306574 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Muscle tissue | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Musculature | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Striated muscle tissue | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |