Spindle cell rhabdomyosarcoma
Spindle cell rhabdomyosarcoma
Definition
An uncommon variant of rhabdomyosarcoma characterized by the presence of whorls of spindle cells forming a storiform pattern. In children it usually arises in the paratesticular region. In adults it usually arises from the deep soft tissues in the head and neck.
Also known as spindle cell rhabdomyosarcoma (morphologic abnormality) — per MONDO
Also identified as
- DOID 3260 per MONDO
- ICD9 171.9 per MONDO
- NCIT C6519 per MONDO
- SCTID 404055006 per MONDO
- UMLS C1266134 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Muscle tissue | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Musculature | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Striated muscle tissue | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |