Extramedullary plasmacytoma
Extramedullary plasmacytoma
Definition
A plasma cell neoplasm arising at an extraosseous site. There is no involvement of the bone marrow. It most frequently involves the oropharynx, nasopharynx, sinuses, and larynx. Other sites of involvement include the gastrointestinal tract, central nervous system, breast, skin, lymph nodes, and bladder. A minority of patients have a monoclonal gammopathy. Treatment includes radiation therapy. Progression to plasma cell myeloma occurs in a minority of patients.
Also known as extramedullary plasmacytoma, extramedullary plasmacytoma (clinical), extraosseous plasmacytoma, plasmacytoma, extramedullary, plasmacytoma, extramedullary (not occurring in bone) — per MONDO
Also identified as
- DOID 3720 per MONDO
- ICD10CM C90.2 per MONDO
- ICD9 203.80 per MONDO
- NCIT C4002 per MONDO
- SCTID 188718006 per MONDO
- UMLS C0278619 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Lymphoid system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |