Rhabdomyosarcoma with mixed embryonal and alveolar features

Rhabdomyosarcoma with mixed embryonal and alveolar features

Definition

A rhabdomyosarcoma composed of embryonic and alveolar components. It is characterized by the presence of spindle cells with myoblastic differentiation, a myxoid stroma, and fibrous septa. These tumors were previously considered variants of alveolar rhabdomyosarcoma. The lack of PAX3-FOXO1 fusions in most of these tumors suggests that are biologically and clinically related to embryonal rhabdomyosarcoma.

Also known as mixed alveolar rhabdomyosarcoma, mixed type alveolar rhabdomyosarcoma, rhabdomyosarcoma with mixed embryonal and alveolar features — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Muscle tissue Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Musculature Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Musculoskeletal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Striated muscle tissue Disease Has Primary Anatomic Site NCIT · CC BY 4.0